| Title: |
Experience with etilefrine in refractory non-traumatic chylothorax: a case report |
| Authors: |
Sakai, Ryo; Shiraga, Kazuhiro; Inuzuka, Ryo |
| Source: |
Cardiology in the Young ; volume 35, issue 6, page 1270-1272 ; ISSN 1047-9511 1467-1107 |
| Publisher Information: |
Cambridge University Press (CUP) |
| Publication Year: |
2025 |
| Description: |
Noonan syndrome is associated with lymphatic system structural abnormalities and may present with potentially fatal refractory chylothorax. We report a 2-year-old boy with Noonan syndrome with non-traumatic chylothorax who was refractory to dietary therapy with medium-chain triglyceride milk, octreotide, prednisolone, lymphatic embolisation, and lymphatico-venous anastomosis but improved with etilefrine administration. Etilefrine may be a treatment option for paediatric chylothorax, regardless of the aetiology. |
| Document Type: |
article in journal/newspaper |
| Language: |
English |
| DOI: |
10.1017/s104795112510067x |
| Availability: |
https://doi.org/10.1017/s104795112510067x; https://www.cambridge.org/core/services/aop-cambridge-core/content/view/S104795112510067X |
| Rights: |
https://creativecommons.org/licenses/by/4.0/ |
| Accession Number: |
edsbas.150CBF65 |
| Database: |
BASE |