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International Consensus for the Dosing of Corticosteroids in Childhood-Onset Systemic Lupus Erythematosus With Proliferative Lupus Nephritis

Title: International Consensus for the Dosing of Corticosteroids in Childhood-Onset Systemic Lupus Erythematosus With Proliferative Lupus Nephritis
Authors: Chalhoub, Nathalie E.; Wenderfer, Scott E.; Levy, Deborah M.; Rouster-Stevens, Kelly; Aggarwal, Amita; Savani, Sonia I.; Ruth, Natasha M.; Arkachaisri, Thaschawee; Qiu, Tingting; Merritt, Angela; Onel, Karen; Goilav, Beatrice; Khubchandani, Raju P.; Deng, Jianghong; Fonseca, Adriana R.; Ardoin, Stacy P.; Ciurtin, Coziana; Kasapcopur, Ozgur; Jelusic, Marija; Huber, Adam M.; Ozen, Seza; Klein-Gitelman, Marisa S.; Appenzeller, Simone; Cavalcanti, André; Fotis, Lampros; Lim, Sern Chin; Silva, Rodrigo M.; Miramontes, Julia Ramírez-; Rosenwasser, Natalie L.; Saad-Magalhaes, Claudia; Schonenberg-Meinema, Dieneke; Scott, Christiaan; Silva, Clovis A.; Enciso, Sandra; Terreri, Maria T.; Torres-Jimenez, Alfonso-Ragnar; Trachana, Maria; Al-Mayouf, Sulaiman M.; Devarajan, Prasad; Huang, Bin; Brunner, Hermine I.; Abulaban, Khalid; Aguiar, Cassyanne; Ahn, Sun-Young; Akoghlanian, Shoghik; Al-Abrawi, Safiya; Aljaberi, Najla; Alperin, Risa; Angeles-Han, Sheila; Ardalan, Kaveh; Bader-Meunier, Brigitte; Balboni, Imelda; Barbar-Smiley, Fatima; Baxter, Sarah; Beary, John; Boneparth, Alexis; Brakeman, Paul; Bridges, John; Burgos-Vargas, Ruben; Cabral, David A.; Cameto, Juan; Carter, Caitlin; Chang, Joyce; Chédeville, Gaëlle; Chhakchhuak, Christine; Chiraseveenuprapund, Peter; Cifuentes Alvarado, Mayra; Concannon, Anthony; Cooper, Jennifer; Cron, Randy; De Carvalho, Luciana Martins; De Quattro, Kimberly; De Ranieri, Deirdre; Dizon, Brian; Donnelly Wrigley, Catherine; Duong, Minh Dien; Eberhard, Anne; Ede, Kaleo; Edelheit, Barbara; Edens, Cuoghi; Espada, Graciela; Farhey, Yolanda; Flores, Francisco; Fritz, Deborah; Ganguli, Suhas; Gilbert, Mileka; Gittar, Patsy; Greenbaum, Larry; Grom, Alexei; Gulati, Gaurav; Harry, Onengiya; Hayward, Kristen; Henrickson, Michael; Hersh, Aimee; Hiraki, Linda; Hiskey, Megan; Hoffmann, Sarah; Hollander, Matthew; Hom, Christine; Houk, Lawrence; Houk, J. Brian; Hsieh, Elena W.Y.; Hsu, Joyce; Jensen, Paul; Joos, Rik; Jurado, Rosario; Jusan Fiorot, Fernanda; Kallash, Mahmoud; Kamphuis, Sylvia; Keltsev, Vladimir; Khanna, Surabhi; Kim, Susan; Kimseng, Karen Joy; Knight, Andrea; Kunder, Rebecca; Lai, Jamie; Laskin, Benjamin; Lewandowski, Laura; Lim, Lily; Linda, Wagner-Weiner; Lo, Mindy; Lovell, Daniel; Luggen, Michael; Madison, Jacqueline; Mansuri, Asif; Martin, Lorena; Mason, Sherene; Miller, Michael; Mina, Rina; Mohammed, Abdul; Moncrieffe, Halima; Moorthy, Lakshmi; Morgan, Esi; Mosquera, Angela; Muntel, Emily; Muscal, Eyal; Myones, Barry; Nocton, James; Ogbu, Ekemini; Okamura, Daryl; Olson, Judyann; Orrock, Janet; Paim-Marques, Luciana; Pain, Clare; Park, Catherine; Patel, Pooja; Pereira, Maria; Prado, Rogerio do; Radhakrishna, Suhas; Rheault, Michelle; Ridgway, William; Riskalla, Mona; Ronis, Tova; Sadun, Rebecca; Sagcal-Gironella, Anna Carmela; Santos, Maria carolina; Schikler, Kenneth; AL Suwairi, Wafaa; Siddiqi, Nabeela; Silva, Marco Felipe; Singh-Grewal, Davinder; Smitherman, Emily; Smolewska, Elzbieta; Son, Mary Beth; Srinivasalu, Hemalatha; Sule, Sangeeta; Susic, Gordana; Syed, Reema; Thatayatikom, Akaluck; Ting, Tracy; Toth, Mary; Turnier, Jessica; Vashisht, Priyanka; Vega Fernandez, Patricia; Velasquez, Monica; von Scheven, Emily; Wahezi, Dawn; Ware, Avis; Wu, Eveline; Yan, Jacqueline; Yildirim-Toruner, Cagri; Zamparo, Celso; Zhang, Yujuan; Lawson, Erica
Contributors: Universidade Estadual Paulista (UNESP)
Publication Year: 2022
Collection: Universidade Estadual Paulista São Paulo: Repositório Institucional UNESP
Description: Arthritis Foundation ; Institute of Clinical and Translational Sciences ; Conselho Nacional de Desenvolvimento Científico e Tecnológico (CNPq) ; Fundação de Amparo à Pesquisa do Estado de São Paulo (FAPESP) ; National Institute of Arthritis and Musculoskeletal and Skin Diseases ; National Institute of Diabetes and Digestive and Kidney Diseases ; National Center for Advancing Translational Sciences ; CNPq: 303422/2015-7 ; Processo FAPESP: FAPESP 2015/03756-4 ; National Institute of Arthritis and Musculoskeletal and Skin Diseases: P30-AR-076316 ; National Institute of Diabetes and Digestive and Kidney Diseases: P50-DK-096418 ; National Institute of Arthritis and Musculoskeletal and Skin Diseases: R34-AR-071651 ; National Center for Advancing Translational Sciences: T32-AR-050958 ; Objective: To develop a standardized steroid dosing regimen (SSR) for physicians treating childhood-onset systemic lupus erythematosus (SLE) complicated by lupus nephritis (LN), using consensus formation methodology. Methods: Parameters influencing corticosteroid (CS) dosing were identified (step 1). Data from children with proliferative LN were used to generate patient profiles (step 2). Physicians rated changes in renal and extrarenal childhood-onset SLE activity between 2 consecutive visits and proposed CS dosing (step 3). The SSR was developed using patient profile ratings (step 4), with refinements achieved in a physician focus group (step 5). A second type of patient profile describing the course of childhood-onset SLE for ≥4 months since kidney biopsy was rated to validate the SSR-recommended oral and intravenous (IV) CS dosages (step 6). Patient profile adjudication was based on majority ratings for both renal and extrarenal disease courses, and consensus level was set at 80%. Results: Degree of proteinuria, estimated glomerular filtration rate, changes in renal and extrarenal disease activity, and time since kidney biopsy influenced CS dosing (steps 1 and 2). Considering these parameters in 5,056 patient profile ratings from 103 ...
Document Type: article in journal/newspaper
File Description: 263-273
Language: English
ISSN: 2326-5205; 2326-5191
Relation: Arthritis and Rheumatology; http://dx.doi.org/10.1002/art.41930; Arthritis and Rheumatology, v. 74, n. 2, p. 263-273, 2022.; http://hdl.handle.net/11449/223171; 2-s2.0-85122264560
DOI: 10.1002/art.41930
Availability: http://hdl.handle.net/11449/223171; https://doi.org/10.1002/art.41930
Accession Number: edsbas.1E765213
Database: BASE