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Program and abstracts for the 2012 Joint Meeting of the Society for Glycobiology & American Society for Matrix Biology

Title: Program and abstracts for the 2012 Joint Meeting of the Society for Glycobiology & American Society for Matrix Biology
Authors: Schnaar, Ronald; Paulson, James C; Macauley, Matthew S.; Nycholat, Corwin; Pfrengle, Fabian; Rademacher, Christoph; Mahan, Alison; Dionne, Kendall; Suscovich, Todd; Alter, Galit; Katoh, Toshihiko; Kiwamoto, Takumi; Brummet, Mary; Bochner, Bruce; Tiemeyer, Michael; Aquino, Rafael; Liu, Jian; Park, Pyong Woo; Soto-Pantoja, David; Miller, Thomas; Pendrak, Michael; DeGraff, William; Sullivan, Camille; Ridnour, Lisa; Abu-Asab, Mones; Wink, David; Tsokos, Maria; Roberts, David; Ihara, Yoshito; Ikezaki, Midori; Inai, Yoko; Matsui, In-Sook; Muroi, Eiji; Shibukawa, Yukinao; Wada, Yoshinao; Manabe, Shino; Ito, Yukishige; Rivera, Lee; Carbon, Juliet; Toombs, Jason; Aguilera, Kristina; Chakrabarti, Gaurab; Braunfeld, Jordan; Brekken, Rolf; Combs, Michelle D.; Knutsen, Russell H.; Broekelmann, Thomas J.; Toennies, Holly M.; Brett, Thomas J.; Craft, Clarissa S.; Atkinson, Jeffrey J.; Shipley, Michael J.; Mecham, Robert P.; Lee, Albert; Miller, Devin; Henry, Roger; Zachara, Natasha; Weinbaum, Justin; Schmidt, Jill; Tranquillo, Robert; Secundino-Vélazquez, Ismael; Wang, Xiaoxia; Roupé, K Markus; Varki, Ajit; Nizet, Victor; Jeanne, Marion; Jorgensen, Jeff; Labelle-Dumais, Cassandre; Weng, Yi-Chinn; Kauffman, W Berkeley; de Leau, Michelle; Greenberg, Steven M; Rosand, Jonathan; Favor, Jack; Gould, Douglas B; Kang, Inkyung; Yoon, Dong; Braun, Kathleen; Wight, Thomas; Wohl, Alexander; Zuk, Alexandra; Sakai, Lynn; Sengle, Gerhard; Willer, Tobias; Lee, Hane; Lommel, Mark; Yoshida-Moriguchi, Takako; de Bernabe, Daniel Beltran Valero; Venzke, David; Cirak, Sebahattin; Schachter, Harry; Vajsar, Jiri; Voit, Thomas; Muntoni, Francesco; Strahl, Sabine; Mathews, Katherine D.; Nelson, Stanley F.; Moore, Steven A.; Campbell, Kevin P.; Aoki, Kazuhiro; Boccuto, Luigi; Kulik, Michael; Flanagan-Steet, Heather; Schwartz, Charles; Dalton, Stephen; Steet, Richard; Coles, Chantal; Hunt, Liam; Piers, Adam; McCulloch, Daniel; Stupka, Nicole; Lamande, Shireen; White, Jason; Pokidysheva, Elena; Boudko, Sergei; Vranka, Janice; Keene, Douglas; Tufa, Sara; Zentek, Keith; Moser, Marcus; Faessler, Reinhard; Ware, Jerry; Bächinger, Hans Peter; Cook, Jason; Carta, Luca; Benard, Ludovic; Chemaly, Elie; Chiu, Emily; Hampton, Tom; Clayton, Nicholas; Nelson, Carol; Wentworth, Bruce; Hajjar, Roger; Ramirez, Francesco; Miner, Jeffrey; Lin, Xiaobo; Witzenman, Hilary; Lyalin, Dmitry; Caster, Courtney; Nakamura, Michiko; Kc, Niraj; Islam, Rafique; Zoran, Mark; Panin, Vladislav; Mi, Rongjuan; Song, Lina; Wang, Yingchun; Ding, Xiaokun; Zeng, Junwei; Arayl, Rajindra P.; Crew, Vanja K.; van Die, Irma; Chapman, Arlene B.; Cummings, Richard D.; Ju, Tongzhong; Gordts, Philip L.S.M.; Foley, Erin; Lawrence, Roger Lawrence; Erbilgin, Ayca; Lusis, Aldons J.; Witztum, Jozef; Esko, Jeffrey D.; Goldoni, Silvia; von Erlach, Thomas; Platt, Randall; Arnoldini, Simon; Chen, Xinyong; Stevens, Molly; Hubbard, Brant; Nugent, Matt; Smith, Michael; Buczek-Thomas, Jo Ann; Peters, Sarah; Naim, Nyla; Mosier, Aaron; Nelson, Deirdre; Cady, Nathaniel; Larsen, Melinda; López-Alpuche, Vanessa; Honkanen, Hanne-Kaisa; Seppinen, Lotta; Kinnunen, Aino; Elamaa, Harri; Mäkinen, Markus; Eklund, Lauri; Heljasvaara, Ritva; Pihlajaniemi, Taina; Malara, Alessandro; Currao, Manuela; Gruppi, Cristian; Balduini, Alessandra; Xin, Wei; Paulsson, Mats; Zaucke, Frank; Baum, Linda G; Thiemann, Sandra; Clark, Mary; Pang, Mabel; Swindall, Amanda F; Londoño-Joshi, Angelina I; Buchsbaum, Donald J; Bellis, Susan L; Holle, Andrew; Tang, Xinyi; Engler, Adam; Frand, Alison; Bourhis, Jean-Marie; Mariano, Natacha; Goff, Sandrine Vadon-Le; Afrache, Hassnae; Zhao, Yuguang; Harlos, Karl; Exposito, Jean-Yves; Jones, Yvonne; Aghajari, Nushin; Moali, Catherine; Hulmes, David; Petrosyan, Armen; Ali, Mohamed; Cheng, Pi-Wan; Singh, Purva; Schwarzbauer, Jean E.; Ruan, Jian; Nan, Li; Javed, Amjad; Purushothaman, Anurag; Sanderson, Ralph D; Suva, Larry J.; Yang, Yang; Zoeller, Jason; Bronson, Roderick; Gilmer, Tona; Selfors, Laura; Lu, Yiling; Apple, Sophia; Press, Michael; Hurvitz, Sara; Slamon, Dennis; Mills, Gordon; Brugge, Joan; Naba, Alexandra; Clauser, Karl; Carr, Steven; Hynes, Richard; Neelamegham, Sriram; Lo, Chi; Antonopoulos, Aristotelis; Dell, Anne; Haslam, Stuart; Bovin, Nicolai; Henry, Stephen; Korchagina, Elena; Tuzikov, Alexander; Samli, Kausar N.; Yang, Loretta; Woods, Robert J.; Stanley, Pamela; Batista, Frank; Huang, Hung-Hsiang; Lu, Linchao; Williams, Suzannah A.; Hubmacher, Dirk; Wang, Lauren W; Mecham, Robert P; Reinhardt, Dieter P; Apte, Suneel S; Petrey, Aaron; Sahu, Sanjukta; Marshall, Marion; Santayana, Christine; Nishihara, Shoko; Ang, Lisa; Boivin, Wendy; Zhao, Hongyan; Chu, Fanny; Bleackley, R Chris; Granville, David; Zimmerman, Kurt; Gamlin, Clare; Pallero, Manuel; Murphy-Ullrich, Joanne; Crosson, Stephanie; McKee, Karen; Ruegg, Markus; Yurchenco, Peter; Han, Liang; Costello, Catherine E.; Ruhaak, L Renee; Stroble, Carol; Lebrilla, Carlito B; Miyamoto, Suzanne; Fischer, Kathleen; Stein, Karina; Lindner, Buko; Heine, Holger; Holst, Otto; Kannan, Arthi; Wang, Ying-Ying; Subramani, Durai; Murphy, Michael; Nunn, Kenetta; Moench, Thomas; Cone, Richard; Lai, Samuel; Avci, Fikri Y; Li, Xiangming; Tsuji, Moriya; Kasper, Dennis; Chang, Yung-Chi; Olson, Joshua; Tung, Christine; Zhang, Jiquan; Crocker, Paul; Liu, Zhongyu; Swindall, Amanda; Schultz, Matthew; Bullard, Daniel; Bellis, Susan; Bergfeld, Anne K; Diaz, Sandra L; Lawrence, Roger; Pearce, Oliver MT; Esko, Jeffrey D; Bollyky, Paul; Falk, Ben; Pickett, Melissa; Nepom, Gerald; Chiang, Meng-Lin; Chiang, Po-Cheng; Hsu, Daniel; Liu, Fu-Tong; Chen, Huan-Yuan; Date, Kimie; Kawasaki, Nana; Hashii, Noritaka; Sakagami, Hiromi; Ogawa, Haruko; Ulm, Christina; Saffarzadeh, Mona; Mahavadi, Poornima; Geyer, Hildegard; Müller, Sandra; Prem, Linda; Bayer, Nils; Simon, Peter; Sabor, Farhan; Middendorff, Ralf; Rinné, Susanne; Lütteke, Thomas; Böttcher-Friebertshäuser, Eva; Gerardy-Schahn, Rita; Mühlenhoff, Martina; Preissner, Klaus T.; Günther, Andreas; Geyer, Rudolf; Galuska, Sebastian P.; Hudson, Sherry; Motari, Mary; Zhu, Zhou; Mickum, Megan L; Dorabawila, Nelum; Heimburg-Molinaro, Jamie; Lasanajak, Yi; Mandalasi, Msano; Song, Xuezheng; Smith, David F; Nyame, A Kwame; Cummings, Richard D; Newburg, David S.; Yu, Zhuoteng; Taft, Diana; Lagomarcino, Anne; Schibler, Kurt R.; Givers, Dirk; Ward, Doyle; Morrow, Ardythe L.; Padler-Karavani, Vered; Deng, Liwen; Garcia, Andrea; Karp, Felix; Naidu, Natasha; Choudhury, Biswa; Varki, Nissi; Shah, Nikunj; Hülsmeier, Andreas; Hennet, Thierry; Spiller, Fernando; Silva, Frederico; Previato, José; Previato, Lúcia; Todeschini, Adriane; Cunha, Fernando; Man, Jeanette; Baum, Linda; Hu, Huifeng; Wei, Yadong; Fernandes, Steve M; Gil, Anabel Gonzales; Schnaar, Ronald L; Aguilera, Kristina Y; Goldstein, Courtney D; Rivera, Lee B; Bradshaw, Amy D; Brekken, Rolf A.; Alford, Andrea; Reddy, Anita; Broekelmann, Thomas; Combs, Michelle; Craft, Clarissa; Mecham, Robert; Hanisch, Franz-Georg; Breloy, Isabelle; Bonar, David; Huang, Lei; Jadin, Laurence; Zhao, Qiping; Wei, Gina; Jiang, Ping; Shepard, Michael; Kwon, Doo Yeon; Yoon, So Mi; Kim, Da Yeon; Seo, Hyo Won; Kwon, Jin Seon; Kim, Young Jick; Kim, Jae Ho; Kim, Moon Suk; Tran, Duy; Lim, Jae-Min; Liu, Mian; Stalnaker, Stephanie; Wells, Lance; Ten Hagen, Kelly; David, Live; Mao, Yang; Huang, Yu; Wu, Zhengliang; Zaia, Joseph; Penm, Steven; Lord, Megan; O'Grady, Robert; Whitelock, John; Coustry, Francoise; Posey, Karen; Liu, Peiman; Veerisetty, Alka; Alcorn, Joseph; Hecht, Jacqueline; Rohani, Maryam G; Harkavy, Shula; Parks, William C; Sim, Sun Woo; KIM, Jae Ho; Min, Byoung Hyun; Stacey, Michael; Asmar, Anthony; Pakhomova, Olga; Kelly, Robert; Tai, GuoZhe; Lee, Hai Bang; Tsunezumi, Jun; Yanagisawa, Hiromi; Lu, Hang; Wang, Qiukuan; Zhang, Li; Hu, Jianen; Wulf-Johansson, Helle; Rasmussen, Lars Melholt; Tornøe, Ida; Marcussen, Niels; Nielsen, Ole; Holmskov, Uffe; Sorensen, Grith Lykke; Abdulkhalek, Samar; Szewczuk, Myron; Alghamdi, Farah; Cecílio, Nerry; Luche, Douglas; Carvalho, Fernanda; Fernandes, Andre; Liu, Yan; Feizi, Ten; Goldman, Maria Helena; Roque-Barreira, Maria Cristina; Cecilio, Nerry; Ma, Fang; Wu, Diana; Sroga, Julie; Whigham, Leah; Lindheim, Steven; Gagneux, Pascal; Goodwin, Octavia; Macnaughtan, Megan; Bond, Michelle; Ghosh, Salil; Krause, Michael; Hanover, John; Hart, Gerald; Munteanu, Cristina; Condac, Eduard; Ferencz, Beatrix; Silasi-Mansat, Robert; Lupu, Florea; Hinsdale, Myron E; Hsieh, Shie-Liang; Arnaud, Julie; Audfray, Aymeric; Claudinon, Julie; Römer, Winfried; Varrot, Annabelle; Imberty, Anne; Katai, Emese; Pal, Jozsef; Nagy, Tamas; Miseta, Attila; Kovacs, Gabor L.; Maverick, Emily; Sweeney, Michelle; Buffone, Alexander; Mondal, Nandini; McHugh, Kyle; Lau, Joseph; Newburg, David S; Meng, Di; Nanthakumar, Nanda; Nishida, Mitsutaka; Nagami, Keitaro; Kanamaru, Yoshihiro; Yabe, Tomio; Yurdagul, Arif; Chen, Jie; Funk, Steven; Albert, Patrick; Kevil, Christopher; Orr, Wayne; Reeves, Russell; Sardinha-Silva, Aline; Lopes, Carla D; Ruas, Luciana P; Gay, Nicholas; Almeida, Igor C; Pinzan, Camila F; Kumar, Archana Vijaya; Gassar, Ezeddin Salem; Spillman, Dorothe; Stock, Christian; Kiesel, Ludwig; Yip, George; Goette, Martin; Xu, Ding; Young, Jeffrey; Chazin, Walter; Esko, Jeffrey; Andrie, Rachael M.; Manalo, Elise C.; Gonzalez, Sara Tufa; Charbonneau, Noe L.; Keene, Doug R.; Sakai, Lynn Y.; Carlson, Eric; Charbonneau, Noe; Andrie, Rachael; Saka, Lynn; del Solar, Maria; Lindsay, Mark; Dietz, Harry; Du, Yaoyao; Hatakeyama, Shingo; Tobisawa, Yuki; Yoneyama, Tohru; Amano, Maho; Nishimura, Shin-Ichiro; Ohyama, Chikara; Hirohata, Satoshi; Ohtsuki, Takashi; Obika, Masanari; Ogawa, Hiroko; Kusachi, Shozo; Ninomiya, Yoshifumi; Tufa, Sara F; Sakai, Lynn Y; Keene, Douglas R; Khatri, Sandeep; Maxfield, Andrew; Joseph, Elaine; Urban, Zsolt; Krishnamurthy, Varun; Wansapura, Janaka; Evans, Ashlie; Maddy, Kelsey; Biechler, Stefanie; Goodwin, Richard; Narmoneva, Daria; Hinton, Robert; Kuranami, Yumiko; Takaya, Shoko; Hagiuda, Ayano; Kojima-Aikawa, Kyoko; Manalo, Elise; Keene, Doug; Mizuno, Kazunori; Engel, Jürgen; Nakamura, Tomoyuki; Noel, Onika; Turlo, Kirsten; Iruela-Arispe, Luisa; Pan, Yanfang; Yago, Tadayuki; Xia, Lijun; Sabatier, Laetitia; Hassan, Amani; Fagotto-Kaufmann, Christine; Sakai, Takao; Reinhardt, Dieter; Wang, Zhepeng; Bryan, Jennifer; Sandell, Linda; Scott, David; Patel, Rakesh; Chacko, Balu; Traylor, Robert; Nambu, Satoko; Takeda, Risako; Su, Chi-Ting; Weckenmann, Christine; Lawrence, Elizabeth; He, Yunhai; Ren, Dandan; Hui, Fu; Yu, Xingju; Yamashiro, Yoshito; Huang, Jianbin; Mirzaei, Hamid; Henry, Michael D.; DeRossi, Charles; Thiel, Christian; Ichikawa, Mie; Sharma, Vandana; Hoffman, Georg F.; Freeze, Hudson H.; Körner, Christian; Wang, Aimin; Hascall, Vincent; Losfeld, Marie-Estelle; Lehoux, Sylvain; Aryal, Rajindra; Schjoldager, Katrine T.B.G.; Clausen, Henrick; Longas, Maria O; Archer-Hartmann, Stephanie A; Azadi, Parastoo; Nagy, Nadine; Kaber, Gernot; Campbell, Daniel J.; Wight, Thomas N.; Sano, Kotone; Sobukawa, Naomi; Asanuma-Date, Kimie; Orgel, Joseph; Madhurapantula, Rama; Antipova, Olga; Pereira, Natasha; Pu, Helen; Song, Zhiwei; Seamen, Emylie; Nora, Chelsea L.; Sinha, Risha; Nayak,, Jonamani; Smolin,, Jamie; King, Emily M; Holt, Rochelle M; Ballingerand, Elaine; Kashyap, Purna; Sonnenburg, Justin L; Ayala, Julio E; Freeze, Hudson H; da Silva, Frederico Alisson; de Lima, Leonardo Freire; Penha, Luciana; Lucena, Miguel; Donadio, Joana Laureano; Dias, Wagner Barbosa; Barnes, Jarrod; Simpliciano, Jennifer; Hosono-Fukao, Tomomi; Ohtake-Niimi, Shiori; Hoshino, Hitomi; Wyss-Coray, Tony; Uchimura, Kenji; Veillon, Lucas; Ishihara, Mayumi; Lau, Joseph TY; Nasirikenari, Mehrab; Wiederschain, Gherman; Mori, Kazuyuki; Yamamoto, Hayato; Okamoto, Teppei; Okamoto, Akiko; Ishimura, Fumihiro; Yoneyama, Takahiro; Koie, Takuya; Kamimura, Noritaka; Steplewski, Andrzej; Kasinskas, Anthony; Fertala, Jolanta; Fertala, Andrzej; Kuo, Debbie; Mao, Mao; Kauffman, Berkeley; Allen, Jennifer; Gould, Douglas; Greciano, Patricia G.; Buschmann, Mary M.; Hendin, Josh O.; Myllymäki, Satu M.; Manninen, Aki; Moyano, Jose V.; Matlin, Karl S.; Inamori, Kei-ichiro; Hara, Yuji; Anderson, Mary; Yu, Liping; Campbell, Kevin; Hendin, Joshua O.; Teräväinen, Terhi P.; Ray, Shayoni; Fanti, Joseph; Robertson, Wesley E; Rose, Kristie L; Rafi, Mohamed; Hudson, Billy G; Vanacore, Roberto M; Gahlay, Gagandeep; Moremen, Kelley; Steel, Jason; LaBaer, Joshua; Jarvis, Donald; Geisler, Christoph; Grassot, Vincent; Dupuy, Fabrice; Da Silva, Anne; Maftah, Abderrahman; Petit, Jean-Michel; Kizuka, Yasuhiko; Okahara, Kyohei; Kitazume, Shinobu; Taniguchi, Naoyuki; Cascio, Leandro Lo; Lim, Ngee Han; Layyous, Andrea; Liu, Ke; Nakamura, Hiroyuki; Saklatvala, Jeremy; Bou-Gharios, George; Moremen, K.W.; Strachan, H.; Ramiah, A.; Johnson, R.; Meng, L.; Gao, Z.; Nairn, A.V.; Xiang, Y.; Rosa, M. dela; Jarvis, D.; Steel, J.; LaBaer, J.; Ng, Bobby G.; Raymond, Kimiyo; Patterson, Marc C.; Losfeld, Marie Estelle; He, Ping; Eroshkin, Alexey M.; Shrimal, Shiteshu; Gilmore, Reid; Parreno, Justin; Andrejevic, Katarina; Kandel, Rita; Tsai, Yi-Tzang; Yu, Robert; An, Bo; Bradshaw, Mark; Canovic, Elizabeth; Seidl, Tom; Oberai, Assad; Barbone, Paul; Stamenovic, Dimitrije; Culpepper, Bonnie; Prevelige, Peter; Morris, David; Ponnazhagan, Selvarangan; Levy, Seth; Reddy, Michael; Hoffman, Brenton; Grashoff, Carsten; Schwartz, Martin; Mabashi-Asazuma, Hideaki; Toth, Ann; Khan, Aamer; Khan, Aasma; Lee, Robert; Urban, Jill; Jayes, Friederike; Brimmer, Courtney; Leppert, Phyllis; Mack, Julia; Youssef, Khalid; Lake, Michael; Wu, Ashley; Bouchard, Louis; Meredith, Anna; Abraham, Thomas; McManus, Bruce; Nomizu, Motoyoshi; Yamada, Yuji; Katagiri, Fumihiko; Hozumi, Kentaro; Kikkawa, Yamato; Nishida, Keiichiro; Petrie, Ryan; Yamada, Kenneth; Phipps, Matthew; Xu, Yuanyuan; Polio, Samuel; Sachar, Ashneet; Strom, Amanda; Serrano, Maria; Svoboda, Kathy KH; Liu, Xiaohua; Swarup, Vimal; Hsiao, Tony; Zhang, Jianxing; Prestwich, Glenn; Hlady, Vladimir; Kuberan, Balagurunathan; Vincent, Ludovic; Tay, Chor Yong; Carlos del Alamo, Juan; Poh Tan, Lay; Hedegaard, Martin; Wen, Jessica; Karpiak, Jerome; Almutairi, Adah; Wolf, Matthew; Daly, Kerry; Brennan-Pierce, Ellen; Johnson, Scott; Carruthers, Christopher; D'Amore, Antonio; Nagarkar, Shailesh; Velankar, Sachin; Badylak, Stephen; Young, Jennifer; Kretchmer, Kyle; Schaefer, Jacquelyn; Ashby, William; Wikswo, John; Zijlstra, Andries; Zimina, Elena; Clement, Sophie; Bruckner-Tuderman, Leena; Has, Cristina; Hinz, Boris; Addington, Caroline; Pauken, Christine; Caplan, Michael; Stabenfeldt, Sarah; Choi, Yu Suk; Lee, Andrew; Dobke, Marek; Chirasatitsin, Somyot; Viwanathan, Priyalakshmi; Battaglia, Giuseppe; FORGET, Aurelien; Christensen, Jon; Kohler, Esther; Shastri, V. Prasad; Fujiwara, Hironobu; Watt, Fiona; Hadley, Erik B; Norberg, Jessica C; Chan, Mandy M; Wong, Matthew K; Ng, Alvin; Drew, Heather; Miller, Cindy; Eaves, Allen C; Thomas, Terry E; Louis, Sharon A; Hoffman, Matthew; Kim, SangHeon; McDevitt, Todd C.; Nair, Rekha; Fridley, Krista M.; Cooke, Marissa T.; Lynch, Hilary; Kinney, Melissa A.; Ngangan, Alyssa V.; Nairn, Alison; Rosa, Mitche dela; Menendez, Laura; Pierce, Michael; Alisson da Silva, Frederico; de Carvalho Rodrigues, Deivid; Vairo, Leandro; Barbosa Dias, Wagner; Silva, Rosane; Rondinelli, Edson; Carlos Campos de Carvalho, Antonio; Goldemberg, Regina; Urmenyi, Turan; Smaldone, Silvia; Taylor-Weiner, Hermes; Schwarzbauer, Jean; Wang, Yu-Chieh; Sabatini, Karen; Fracchia, Kelley; Slavin, Ileana; Liao, Xiaoyan; Tran, Ha; Leonardo, Trevor; Peterson, Suzanne; Laurent, Louise; Loring, Jeanne; Wong, Simon; Hagood, James; Boudko, Sergei P.; Chachadi, Vishwanath; Cummings, Christopher; Bhave, Gautam; Vanacore, Roberto; Hudson, Billy; Fujita, Morihisa; Lee, Gun-Hee; Murakami, Yoshiko; Maeda, Yusuke; Kinoshita, Taroh; Gaunitz, Stefan; Greenspan, Daniel; Yang, Chenxi; Davis, Nicholas; Park, Arick; Russell, Jason; Coon, Joshua; Hansen, Uwe; Wang, Lei; Bruckner, Peter; Ho, Leona TY; Akama, Tomoya; Koizumi, Noriko; Hosomi, Akira; Suzuki, Tadashi; Hudson, David; Weis, MaryAnn; Wu, Jiann-Jiu; Eyre, David; Khosravi, Roozbeh; Sodek, Katharine; Trackman, Philip; Kopanska, Katarzyna S; Jugdaohsingh, Ravin; Powell, Jonathan J; Bruggraber, Sylvaine FA; Jarvis, Donald L.; Ravindran, Soumya; Wirthlin, Louisa; Lewis, Renate; Traeger, Geoffrey; Fernandes, Russell; McAlinden, Audrey; Muindi, Karen; Vann, Willie; Nakayama, Yoshiaki; Nakamura, Naosuke; Kurosaka, Akira; Harris, Annastasia; Thelen, Ashley; Farmer, Erin; Easley, Katherine; van Lammeren, Kristy; Christoffels, Vincent; Bakkers, Jeroen; Barycki, Joseph; Simpson, Melanie; Jensen, Deborah; Gawron, Katarzyna; Wang, Lauren; Annis, Douglas; Mosher, Deane; Mechan, Robert; Apte, Suneel; Watanabe, Hideto; Ogawa, Hiroyasu; Shionyu, Masafumi; Sugiura, Nobuo; Hatano, Sonoko; Nagai, Naoko; Sato, Takashi; Narimatsu, Hisashi; Shimizu, Katsuji; Kimata, Koji; Kaur, Parminderjeet; Strawn, Rebecca; Matsui, Hiroshi; Xu, Yujia; Zhou, Hui; Froehlich, John; Lee, Richard; Brewer, Fred; Agarwal, Akhil Kumar; Godbole, Rashmi; Srinivasan, Nithya; Kalraiya, Rajiv; Fuhrmann, Alexander; Tlsty, Thea; Hwa, KuoYuan; Liu, Hsuan-Chen; Tanimizu, Naoki; Miwa, Takahiro; Mizuguchi, Toru; Hirata, Koichi; Mitaka, Toshihiro; Liang, Yuh-Jin; Levery, Steven; Handa, Kazuko; Hakomori, Sen-itiroh; Neill, Thomas; Owens, Rick; Baffa, Raffaele; Iozzo, Renato; Wade, Anna; Robinson, Aaron; Engler, Jane; James, C. 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Publisher Information: Oxford University Press
Publication Year: 2012
Collection: HighWire Press (Stanford University)
Subject Terms: ABSTRACTS
Description: Vertebrate cell surfaces feature a rich glycan coat comprised of glycoproteins, glycolipids and proteoglycans. Glycoproteins and glycolipids are often terminated with sialic acid ( N -acetylneuraminic acid, NeuAc), a favored component of larger glycan determinants involved in cell–cell recognition. Sialic acid-dependent binding proteins on one cell engage sialoglycans on an apposing cell to initiate cell–cell recognition. Siglecs—sialic-acid-binding immunoglobulin-like lectins—are a family of 14 sialic acid binding proteins in humans. They are expressed distinct sub-populations of blood cells, except Siglec-4 (myelin-associated glycoprotein, MAG), which is expressed only in the nervous system on the inner-most wrap of myelin, directly across from nerve cell axons. MAG binds preferentially to the “NeuAcα2-3Galβ1-3GalNAc” sequence prominent on two major sialoglycans widely distributed in the vertebrate brain - gangliosides GD1a and GT1b. Direct binding identifies GD1a and GT1b as MAG counter-receptors, and functional studies in vitro and in vivo implicate these gangliosides in maintaining myelin stability, protecting axons from toxic environmental insults and inhibiting axon regeneration after injury. GD1a and GT1b are synthesized by the transfer of sialic acid to the 3-hydroxyl of the terminal galactose of GM1 and GD1b respectively. There are six sialyltransferases in mice and humans that transfer sialic acid to the 3-hydroxyl of galactose, coded by St3gal1 through St3gal6 . We identified St3gal2 and St3gal3 as being responsible for GD1a and GT1b biosynthesis. St3gal2 -null mice express half the GD1a/GT1b of normal mice and have normal sialoglycoprotein levels; St3gal3 -null mice have normal GD1a/GT1b levels, but a 36% decrease in sialic acid on glycoproteins. St3gal2 / St3gal3 -double null mice are essentially devoid of GD1a/GT1b and have half the normal amount of sialic acid on glycoproteins. The double-null mice are growth retarded, have small brains, impaired reflexes and are short-lived. Although required ...
Document Type: text
File Description: text/html
Language: English
Relation: http://glycob.oxfordjournals.org/cgi/content/short/22/11/1518; http://dx.doi.org/10.1093/glycob/cws127
DOI: 10.1093/glycob/cws127
Availability: http://glycob.oxfordjournals.org/cgi/content/short/22/11/1518; https://doi.org/10.1093/glycob/cws127
Rights: Copyright (C) 2012, Society for Glycobiology
Accession Number: edsbas.7B302AAE
Database: BASE