Comparison between idiopathic and VEXAS-relapsing polychondritis: analysis of a French case series of 95 patients
| Title: | Comparison between idiopathic and VEXAS-relapsing polychondritis: analysis of a French case series of 95 patients |
|---|---|
| Authors: | Vincent Jachiet; Benjamin Terrier; Laurence Bouillet; Claire de Moreuil; Joris Galland; Mathilde Devaux; Mathieu Gerfaud-Valentin; Alexandre Maria; Jean Schmidt; Sylvain Audia; Guillaume Denis; Mohamed-Yacine Khitri; Alexis F Guedon; Maelle le Besnerais; Jean Sebastien Allain; Vincent Grobost; Olivier Kosmider; Anael Dumont; Benjamin Subran; Paola Marianetti-Guingel; Sylvain Palat; Marielle Roux-Sauvat; Pierre Hirsch |
| Source: | RMD Open, Vol 8, Iss 2 (2022) |
| Publisher Information: | BMJ Publishing Group |
| Publication Year: | 2022 |
| Collection: | Directory of Open Access Journals: DOAJ Articles |
| Subject Terms: | Medicine |
| Description: | Objective A new adult-onset autoinflammatory syndrome has been described, named VEXAS (Vacuoles, E1 Enzyme, X-linked, Autoinflammatory, Somatic). We aimed to compare the clinical characteristics, the laboratory features and the outcomes between idiopathic-relapsing polychondritis (I-RP) and VEXAS-relapsing polychondritis (VEXAS-RP).Methods Patients from French retrospective multicentre cohort of RP were separated into two groups: a VEXAS-RP and an I-RP.Results Compared with patients with I-RP (n=40), patients with VEXAS-RP (n=55) were men (96% vs 30%, p |
| Document Type: | article in journal/newspaper |
| Language: | English |
| Relation: | https://rmdopen.bmj.com/content/8/2/e002255.full; https://doaj.org/toc/2056-5933; https://doaj.org/article/a959da3d9d8e409592a5aec954add3f0 |
| DOI: | 10.1136/rmdopen-2022-002255 |
| Availability: | https://doi.org/10.1136/rmdopen-2022-002255; https://doaj.org/article/a959da3d9d8e409592a5aec954add3f0 |
| Accession Number: | edsbas.CEE5D59B |
| Database: | BASE |